If the Peters anomaly presents with systemic manifestations like cleft lip/palate, short stature, abnormal ears, and intellectual disability, it is called a Peters plus syndrome. The systemic association is more in type II patients. The term Peters-Plus syndrome was first proposed by VanSchooneveld et al. The lens is cataractous in type II, but it is in the center. In type II, the lens is directly adherent to the posterior corneal opacity. Type II most commonly presents bilaterally. Type II has corneo-lenticular touch or corneal opacity with lens abnormalities. Type I has fewer vitreoretinal and systemic abnormalities as compared to type II. Sometimes peripheral corneal edema or scleralization may also be present. Corneal opacity density varies from mild to severe with a clear peripheral cornea. Type I has iridocorneal adhesion with corneal opacity. Presently Peters anomaly is classified into two types. Type III has central corneal opacity with Rieger mesodermal dysgenesis. Type II presents with corneo-lenticular touch and corneal opacity. Type I involves the cornea alone and presents as a central corneal opacity. classified the Peters anomaly into three types. This iridocorneal adhesion can present as thin filaments, thick bands, or arcuate sheets. In the Peters anomaly, the iridocorneal adhesions typically arise from the collarette and get attached to the margin of the corneal opacity. ![]() ![]() The peripheral cornea is relatively clear, but a variable degree of haze may be associated with central opacity. It is characterized by central corneal opacity of variable size with a corresponding defect in the posterior stroma, Descemet membrane, and endothelium. Peters anomaly is a rare congenital disorder of the anterior segment of the eye.
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